N98

UTERUS AND OVARIES - Hypoplastic

Description
The uterus is very small; the right ovary has been removed entire for histology while the left ovary is represented by a small nodule below the tip of the tube.
History
This woman presented at the age of 37 because her hair was beginning to fall out. She suffered primary amenorrhoea. Laparoscopy showed "streak" ovaries and a small uterus. Her chromosome pattern was XY. It was decided to remove the ovaries because of the risk of development of a gonadoblastoma and the uterus was removed as well to facilitate replacement therapy.